Pattern of inner retinal layers involvement in pigmented paravenous retinochoroidal atrophy as determined by SD-OCT: case report

Pattern of inner retinal layers involvement in pigmented paravenous retinochoroidal atrophy as determined by SD-OCT: case report

Alternative title Padrão de envolvimento das camadas retinianas internas na atrofia retinocoroidiana pigmentada paravenosa determinado pelo SD-OCT: relato de caso
Author Junqueira, Daniela Laura Melo Google Scholar
Lopes, Flavio Siqueira Santos Autor UNIFESP Google Scholar
Biteli, Luis Gustavo Autor UNIFESP Google Scholar
Prata, Tiago dos Santos Autor UNIFESP Google Scholar
Institution Hosp Med Olhos
Universidade Federal de São Paulo (UNIFESP)
Abstract Pigmented paravenous retinochoroidal atrophy is an ocular disease characterized by outer retina and choroidal atrophy often with overlying intraretinal bone spicule pigment deposition along the retinal veins. As a rare condition, there is scant information in the literature regarding the pattern of inner retinal layers involvement. We present a case of a 41-year-old white man initially referred for a glaucoma evaluation. Fundoscopy revealed patches of retinochoroidal atrophy and light pigmentation extending from the optic nerve head along the inferior-temporal retinal veins in both eyes. Using different spectral-domain optical coherence tomography (SD-OCT) protocols we identified a significant thinning of the inner retinal layers along the inferior-temporal veins, but with a lucid interval surrounding the optic nerve head. Standard automated perimetry revealed a superior absolute arcuate scotoma sparing the central fixation (good structure-functional correlation). This pattern of inner retinal layers involvement was not previously described. We believe SD-OCT added significantly to the anatomical description of this case. Physicians should consider these new anatomical findings and correlate them with functional status while assessing these patients.
Keywords Atrophy
Retinal ganglion cells
Choroid/pathology
Retina/pathology
Retinal nerve fiber layer
Tomography, optical coherence
Visual field
Case report
Language English
Date 2013-11-01
Published in Arquivos Brasileiros De Oftalmologia. Sao Paulo: Consel Brasil Oftalmologia, v. 76, n. 6, p. 380-382, 2013.
ISSN 0004-2749 (Sherpa/Romeo, impact factor)
Publisher Consel Brasil Oftalmologia
Extent 380-382
Origin http://dx.doi.org/10.1590/S0004-27492013000600014
Access rights Open access Open Access
Type Article
Web of Science ID WOS:000331655800014
SciELO ID S0004-27492013000600014 (statistics in SciELO)
URI http://repositorio.unifesp.br/11600/42726

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