Pseudomyxoma Peritonei Associated With Primary Mucinous Borderline Tumor of the Renal Pelvicalyceal System

Pseudomyxoma Peritonei Associated With Primary Mucinous Borderline Tumor of the Renal Pelvicalyceal System

Author Rao, Priya Google Scholar
Pinheiro, Nathanael Autor UNIFESP Google Scholar
Franco, Marcello Fabiano de Autor UNIFESP Google Scholar
Ra, Seong Google Scholar
Costa, Henrique de Oliveira Autor UNIFESP Google Scholar
Manzano, Joao Padua Autor UNIFESP Google Scholar
Paner, Gladell P. Google Scholar
Silva, Elvio G. Google Scholar
Amin, Mahul B. Google Scholar
Institution Cedars Sinai Med Ctr
Universidade Federal de São Paulo (UNIFESP)
Hosp Vila Maria
Abstract Primary mucinous cystic neoplasms are extraordinarily rare tumors of the kidney. Herein, we present a case of a 52-year-old man who presented with painless hematuria and mucusuria. The nephrectomy showed a markedly enlarged kidney replaced by a large cystic mass filled with mucin and with almost complete destruction of the renal parenchyma. Histologically, the mass was lined primarily by simple mucinous epithelium and showed foci of adenomatous (borderline) change with focal areas exhibiting intraepithelial carcinoma. No invasion was documented after extensive sampling of the tumor. A pathologic diagnosis of intraepithelial carcinoma arising in a mucinous neoplasm of borderline malignancy was rendered. One year later, the patient presented with pseudomyxoma peritonei. This case illustrates that, in a patient with pseudomyxoma peritonei, the absence of an appendiceal, gastrointestinal, or ovarian primary tumor raises the possibility of a primary neoplasm at an unusual site such as the kidney. (Arch Pathol Lab Med. 2009; 133: 1472-1476)
Language English
Date 2009-09-01
Published in Archives Of Pathology & Laboratory Medicine. Northfield: College Amer Pathologists, v. 133, n. 9, p. 1472-1476, 2009.
ISSN 0003-9985 (Sherpa/Romeo, impact factor)
Publisher College Amer Pathologists
Extent 1472-1476
Access rights Open access Open Access
Type Article
Web of Science ID WOS:000269486600029

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